Sturge-Weber 증후군에 동반된 화염상 모반에서 발생한 화농성 육아종 1 예

Abstract

Port-wine stains(PWS) are congenital vascular birthmarks and usually isolated but may be associated with other vascular malformations. Sturge-Weber syndrome(SWS) is defined as facial PWS in association with an ipsilateral leptomeningeal vascular malformation, atrophy and calcification of the underlying cerebral cortex, epilepsy, mental retardation, contralateral hemiparesis and ipsilateral choroidal vascular lesions with glaucoma. Pyogenic granulomas or other nodular angiomatous lesions may develop within preexistent vascular malformation such as PWS. We describe a 22 year-old man who developed a pyogenic granuloma within an existing facial PWS associated with SWS.